Citation: Ys. Huang et Dt. Chuang, MECHANISM FOR BASAL EXPRESSION OF RAT MITOCHONDRIAL BRANCHED-CHAIN-2-OXO-ACID DEHYDROGENASE, Biochemical journal, 334, 1998, pp. 713-722
Authors:
WYNN RM
DAVIE JR
CHUANG JL
COTE CD
CHUANG DT
Citation: Rm. Wynn et al., IMPAIRED ASSEMBLY OF E1 DECARBOXYLASE OF THE BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE COMPLEX IN TYPE IA MAPLE-SYRUP-URINE-DISEASE, The Journal of biological chemistry, 273(21), 1998, pp. 13110-13118
Citation: Jl. Chuang et al., E2 TRANSACYLASE-DEFICIENT (TYPE-II) MAPLE-SYRUP-URINE-DISEASE - ABERRANT SPLICING OF E2 MESSENGER-RNA CAUSED BY INTERNAL INTRONIC DELETIONSAND ASSOCIATION WITH THIAMINE-RESPONSIVE PHENOTYPE, The Journal of clinical investigation, 100(3), 1997, pp. 736-744
Citation: Ys. Huang et Dt. Chuang, STRUCTURAL ORGANIZATION OF THE RAT BRANCHED-CHAIN 2-OXO-ACID DEHYDROGENASE KINASE GENE AND PARTIAL CHARACTERIZATION OF THE PROMOTER-REGULATORY REGION, Biochemical journal, 313, 1996, pp. 603-609
Citation: Jl. Chuang et al., MAPLE-SYRUP-URINE-DISEASE - THE E1-BETA GENE OF HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE COMPLEX HAS 11 RATHER THAN 10 EXONS, AND THE 3'UTR IN ONE OF THE 2 E1-BETA MESSENGER-RNAS ARISES FROM INTRONIC SEQUENCES, American journal of human genetics, 58(6), 1996, pp. 1373-1377
Authors:
LEUNG PSC
CHUANG DT
WYNN RM
CHA SH
DANNER DJ
ANSARI A
COPPEL RL
GERSHWIN ME
Citation: Psc. Leung et al., AUTOANTIBODIES TO BCOADC-E2 IN PATIENTS WITH PRIMARY BILIARY-CIRRHOSIS RECOGNIZE A CONFORMATIONAL EPITOPE, Hepatology, 22(2), 1995, pp. 505-513
Authors:
CHUANG DT
DAVIE JR
WYNN RM
CHUANG JL
KOYATA H
COX RP
Citation: Dt. Chuang et al., MOLECULAR-BASIS OF MAPLE-SYRUP-URINE-DISEASE AND STABLE CORRECTION BYRETROVIRAL GENE-TRANSFER, The Journal of nutrition, 125(6), 1995, pp. 1766-1772
Authors:
CHUANG JL
DAVIE JR
CHINSKY JM
WYNN RM
COX RP
CHUANG DT
Citation: Jl. Chuang et al., MOLECULAR AND BIOCHEMICAL BASIS OF INTERMEDIATE MAPLE-SYRUP-URINE-DISEASE - OCCURRENCE OF HOMOZYGOUS G245R AND F364C MUTATIONS AT THE E1-ALPHA LOCUS OF HISPANIC-MEXICAN PATIENTS, The Journal of clinical investigation, 95(3), 1995, pp. 954-963
Authors:
DAVIE JR
WYNN RM
MENG MS
HUANG YS
AAHUND G
CHUANG DT
LAU KS
Citation: Jr. Davie et al., EXPRESSION AND CHARACTERIZATION OF BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE KINASE FROM THE RAT - IS IT A HISTIDINE-PROTEIN KINASE, The Journal of biological chemistry, 270(34), 1995, pp. 19861-19867
Citation: Rm. Wynn et al., DIFFERENTIAL PROCESSING OF HUMAN AND RAT E1ALPHA-PRECURSORS OF THE BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX CAUSED BY AN N-TERMINAL PROLINE IN THE RAT SEQUENCE, Biochimica et biophysica acta (G). General subjects, 1201(1), 1994, pp. 125-128
Citation: Rm. Wynn et al., MOLECULAR CHAPERONES - HEAT-SHOCK PROTEINS, FOLDASES, AND MATCHMAKERS, The Journal of laboratory and clinical medicine, 124(1), 1994, pp. 31-36
Citation: Mh. Meng et Dt. Chuang, SITE-DIRECTED MUTAGENESIS AND FUNCTIONAL-ANALYSIS OF THE ACTIVE-SITE RESIDUES OF THE E2 COMPONENT OF BOVINE BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX, Biochemistry, 33(43), 1994, pp. 12879-12885
Citation: Mh. Meng et Dt. Chuang, SITE-DIRECTED MUTAGENESIS AND FUNCTIONAL-ANALYSIS OF THE ACTIVE-SITE RESIDUES OF THE E2 COMPONENT OF BOVINE BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX, Biochemistry, 33(43), 1994, pp. 12879-12885
Citation: Rm. Wynn et al., IN-VITRO RECONSTITUTION OF THE 24-MERIC E2 INNER-CORE OF BOVINE MITOCHONDRIAL BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX - REQUIREMENT FOR CHAPERONINS GROEL AND GROES, Biochemistry, 33(30), 1994, pp. 8962-8968
Citation: Jl. Chuang et al., MOLECULAR-BASIS OF MAPLE-SYRUP-URINE-DISEASE - NOVEL MUTATIONS AT THEE1-ALPHA LOCUS THAT IMPAIR E1(ALPHA(2)BETA(2)) ASSEMBLY OR DECREASE STEADY-STATE E1-ALPHA MESSENGER-RNA LEVELS OF BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE COMPLEX, American journal of human genetics, 55(2), 1994, pp. 297-304
Citation: H. Koyata et al., CORRECTION OF MAPLE SYRUP URINE DISEASE (MSUD) IN CELLS FROM A MENNONITE PATIENT BY RETROVIRAL-MEDIATED GENE-TRANSFER, The FASEB journal, 7(7), 1993, pp. 1276-1276
Citation: Jl. Chuang et al., AP-2 ELEMENTS ARE ESSENTIAL FOR BASAL PROMOTER ACTIVITY OF E1-ALPHA GENE OF HUMAN BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX, The FASEB journal, 7(7), 1993, pp. 1277-1277
Citation: Jr. Davie et al., THE ROLE OF MOLECULAR CHAPERONINS IN FOLDING AND ASSEMBLY OF E1 COMPONENT OF MAMMALIAN BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE (BCKAD)COMPLEX IN ESCHERICHIA-COLI, The FASEB journal, 7(7), 1993, pp. 1279-1279
Citation: H. Koyata et al., STABLE CORRECTION OF MAPLE-SYRUP-URINE-DISEASE IN CELLS FROM A MENNONITE PATIENT BY RETROVIRAL-MEDIATED GENE-TRANSFER, Biochemical journal, 295, 1993, pp. 635-639