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Results: 1-25/42
Authors:
Matsumoto, N
Tamura, S
Moser, A
Moser, HW
Braverman, N
Suzuki, Y
Shimozawa, N
Kondo, N
Fujiki, Y
Citation: N. Matsumoto et al., The peroxin Pex6p gene is impaired in peroxisomal biogenesis disorders of complementation group 6, J HUM GENET, 46(5), 2001, pp. 273-277
Authors:
Suzuki, Y
Shimozawa, N
Orii, T
Tsukamoto, T
Osumi, T
Fujiki, Y
Kondo, N
Citation: Y. Suzuki et al., Genetic and molecular bases of peroxisome biogenesis disorders, GENET MED, 3(5), 2001, pp. 372-376
Authors:
Kaneko, S
Onodera, M
Fujiki, Y
Nagasawa, T
Nakauchi, H
Citation: S. Kaneko et al., Simplified retroviral vector GCsap with murine stem cell virus long terminal repeat allows high and continued expression of enhanced green fluorescent protein by human hematopoietic progenitors engrafted in nonobese diabetic/severe combined immunodeficient mice, HUM GENE TH, 12(1), 2001, pp. 35-44
Authors:
Hamada, H
Yamada, N
Watanabe, H
Okuno, S
Fujiki, Y
Kubo, T
Citation: H. Hamada et al., Hypoechoic hepatomegaly associated with transient abnormal myelopoiesis provides clues to trisomy 21 in the third-trimester fetus, ULTRASOUN O, 17(5), 2001, pp. 442-444
Authors:
Tamura, S
Matsumoto, N
Imamura, A
Shimozawa, N
Suzuki, Y
Kondo, N
Fujiki, Y
Citation: S. Tamura et al., Phenotype-genotype relationships in peroxisome biogenesis disorders of PEX1-defective complementation group 1 are defined by Pex1p-Pex6p interaction, BIOCHEM J, 357, 2001, pp. 417-426
Authors:
Harano, T
Nose, S
Uezu, R
Shimizu, N
Fujiki, Y
Citation: T. Harano et al., Hsp70 regulates the interaction between the peroxisome targeting signal type 1 (PTS1)-receptor Pex5p and PTS1, BIOCHEM J, 357, 2001, pp. 157-165
Authors:
Hamada, H
Fujiki, Y
Obata-Yasuoka, M
Watanabe, H
Yamada, N
Kubo, T
Citation: H. Hamada et al., Prenatal sonographic diagnosis of Beckwith-Wiedemann syndrome in association with a single umbilical artery, J CLIN ULTR, 29(9), 2001, pp. 535-538
Authors:
Fujiki, Y
Yoshikawa, Y
Sato, T
Inada, N
Ito, M
Nishida, I
Watanabe, A
Citation: Y. Fujiki et al., Dark-inducible genes from Arabidopsis thaliana are associated with leaf senescence and repressed by sugars, PHYSL PLANT, 111(3), 2001, pp. 345-352
Authors:
Otera, H
Nishimura, M
Setoguchi, K
Mori, T
Fujiki, Y
Citation: H. Otera et al., Biogenesis of nonspecific lipid transfer protein and sterol carrier protein x - Studies using peroxisome assembly-defective pex cell mutants, J BIOL CHEM, 276(4), 2001, pp. 2858-2864
Authors:
Honsho, M
Fujiki, Y
Citation: M. Honsho et Y. Fujiki, Topogenesis of peroxisomal membrane protein requires a short, positively charged intervening-loop sequence and flanking hydrophobic segments - Study using human membrane protein PMP34, J BIOL CHEM, 276(12), 2001, pp. 9375-9382
Authors:
Fujiki, Y
Ito, M
Nishida, I
Watanabe, A
Citation: Y. Fujiki et al., Leucine and its keto acid enhance the coordinated expression of genes for branched-chain amino acid catabolism in Arabidopsis under sugar starvation, FEBS LETTER, 499(1-2), 2001, pp. 161-165
Authors:
Ghaedi, K
Tamura, S
Okumoto, K
Matsuzono, Y
Fujiki, Y
Citation: K. Ghaedi et al., The peroxin Pex3p initiates membrane assembly in peroxisome biogenesis, MOL BIOL CE, 11(6), 2000, pp. 2085-2102
Authors:
Shimozawa, N
Suzuki, Y
Zhang, ZY
Imamura, A
Ghaedi, K
Fujiki, Y
Kondo, N
Citation: N. Shimozawa et al., Identification of PEX3 as the gene mutated in a Zellweger syndrome patientlacking peroxisomal remnant structures, HUM MOL GEN, 9(13), 2000, pp. 1995-1999
Authors:
Imamura, A
Shimozawa, N
Suzuki, Y
Zhang, ZY
Tsukamoto, T
Fujiki, Y
Orii, T
Osumi, T
Kondo, N
Citation: A. Imamura et al., Restoration of biochemical function of the peroxisome in the temperature-sensitive mild forms of peroxisome biogenesis disorder in humans, BRAIN DEVEL, 22(1), 2000, pp. 8-12
Authors:
Fujiki, Y
Onodera, M
Yamaguchi, T
Osawa, M
Sudo, K
Hamada, H
Ema, H
Shibuya, A
Takiguchi, M
Kubo, T
Nakauchi, H
Citation: Y. Fujiki et al., Dominant expansion of human T cells in non-obese diabetic/severe combined immunodeficiency mice implanted with human bone fragments, EXP HEMATOL, 28(7), 2000, pp. 792-801
Authors:
Fujiki, Y
Ito, M
Nishida, I
Watanabe, A
Citation: Y. Fujiki et al., Multiple signaling pathways in gene expression during sugar starvation. Pharmacological analysis of din gene expression in suspension-cultured cells of Arabidopsis, PLANT PHYSL, 124(3), 2000, pp. 1139-1147
Authors:
Imamura, A
Shimozawa, N
Suzuki, Y
Zhang, ZY
Tsukamoto, T
Fujiki, Y
Orii, T
Osumi, T
Wanders, RJA
Kondo, N
Citation: A. Imamura et al., Temperature-sensitive mutation of PEX6 in peroxisome biogenesis disorders in complementation group C (CG-C): Comparative study of PEX6 and PEX1, PEDIAT RES, 48(4), 2000, pp. 541-545
Authors:
Fujiki, Y
Sato, T
Ito, M
Watanabe, A
Citation: Y. Fujiki et al., Isolation and characterization of cDNA, clones for the E1 beta and E2 subunits of the branched-chain alpha-ketoacid dehydrogenase complex in Arabidopsis, J BIOL CHEM, 275(8), 2000, pp. 6007-6013
Authors:
Okumoto, K
Abe, I
Fujiki, Y
Citation: K. Okumoto et al., Molecular anatomy of the peroxin Pex12p - Ring finger domain is essential for Pex12p function and interacts with the peroxisome-targeting signal type1-receptor Pex5p and a ring peroxin, Pex10p, J BIOL CHEM, 275(33), 2000, pp. 25700-25710
Authors:
Otera, H
Harano, T
Honsho, M
Ghaedi, K
Mukai, S
Tanaka, A
Kawai, A
Shimizu, N
Fujiki, Y
Citation: H. Otera et al., The mammalian peroxin Pex5pL, the longer isoform of the mobile peroxisome targeting signal (PTS) type 1 transporter, translocates the Pex7p center dot PTS2 protein complex into peroxisomes via its initial docking site, Pex14p, J BIOL CHEM, 275(28), 2000, pp. 21703-21714
Authors:
Matsumura, T
Otera, H
Fujiki, Y
Citation: T. Matsumura et al., Disruption of the interaction of the longer isoform of Pex5p, Pex5pL, withPex7p abolishes peroxisome targeting signal type 2 - Study with a novel PEX5-impaired Chinese hamster ovary cell mutant, J BIOL CHEM, 275(28), 2000, pp. 21715-21721
Authors:
Fujiki, Y
Citation: Y. Fujiki, Peroxisome biogenesis and peroxisome biogenesis disorders, FEBS LETTER, 476(1-2), 2000, pp. 42-46
Authors:
Shimozawa, N
Zhang, ZY
Imamura, A
Suzuki, Y
Fujiki, Y
Tsukamoto, T
Osumi, T
Aubourg, P
Wanders, RJA
Kondo, N
Citation: N. Shimozawa et al., Molecular mechanism of detectable catalase-containing particles, peroxisomes, in fibroblasts from a PEX2-defective patient, BIOC BIOP R, 268(1), 2000, pp. 31-35
Authors:
Ghaedi, K
Honsho, M
Shimozawa, N
Suzuki, Y
Kondo, N
Fujiki, Y
Citation: K. Ghaedi et al., PEX3 is the causal gene responsible for peroxisome membrane assembly-defective Zellweger syndrome of complementation group G, AM J HU GEN, 67(4), 2000, pp. 976-981
Authors:
Saito, M
Iwamori, M
Lin, B
Oka, A
Fujiki, Y
Shimozawa, N
Kamoshita, S
Yanagisawa, M
Sakakihara, Y
Citation: M. Saito et al., Accumulation of glycolipids in mutant Chinese hamster ovary cells (Z65) with defective peroxisomal assembly and comparison of the metabolic rate of glycosphingolipids between Z65 cells and wild-type CHO-K1 cells, BBA-MOL C B, 1438(1), 1999, pp. 55-62