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Results: 1-13 |
Results: 13
MOLECULAR PATHOLOGY OF GALACTOSIALIDOSIS IN A PATIENT AFFECTED WITH 2NEW FRAMESHIFT MUTATIONS IN THE CATHEPSIN-A PROTECTIVE PROTEIN GENE
Authors: RICHARD C TRANCHEMONTAGNE J ELSLIGER MA MITCHELL GA POTIER M PSHEZHETSKY AV
Citation: C. Richard et al., MOLECULAR PATHOLOGY OF GALACTOSIALIDOSIS IN A PATIENT AFFECTED WITH 2NEW FRAMESHIFT MUTATIONS IN THE CATHEPSIN-A PROTECTIVE PROTEIN GENE, Human mutation, 11(6), 1998, pp. 461-469
CLONING OF THE CDNA AND GENE ENCODING MOUSE LYSOSOMAL SIALIDASE AND CORRECTION OF SIALIDASE DEFICIENCY IN HUMAN SIALIDOSIS AND MOUSE SM J FIBROBLASTS/
Authors: IGDOURA SA GAFUIK C MERTINEIT C SABERI F PSHEZHETSKY AV POTIER M TRASLER JM GRAVEL RA
Citation: Sa. Igdoura et al., CLONING OF THE CDNA AND GENE ENCODING MOUSE LYSOSOMAL SIALIDASE AND CORRECTION OF SIALIDASE DEFICIENCY IN HUMAN SIALIDOSIS AND MOUSE SM J FIBROBLASTS/, Human molecular genetics, 7(1), 1998, pp. 115-120
MOLECULAR MECHANISM OF LYSOSOMAL SIALIDASE DEFICIENCY IN GALACTOSIALIDOSIS INVOLVES ITS RAPID DEGRADATION
Authors: VINOGRADOVA MV MICHAUD L MEZENTSEV AV LUKONG KE ELALFY M MORALES CR POTIER M PSHEZHETSKY AV
Citation: Mv. Vinogradova et al., MOLECULAR MECHANISM OF LYSOSOMAL SIALIDASE DEFICIENCY IN GALACTOSIALIDOSIS INVOLVES ITS RAPID DEGRADATION, Biochemical journal, 330, 1998, pp. 641-650
CLONING, EXPRESSION AND CHROMOSOMAL MAPPING OF HUMAN LYSOSOMAL SIALIDASE AND CHARACTERIZATION OF MUTATIONS IN SIALIDOSIS
Authors: PSHEZHETSKY AV RICHARD C MICHAUD L IGDOURA S WANG SP ELSLIGER MA QU JY LECLERC D GRAVEL R DALLAIRE L POTIER M
Citation: Av. Pshezhetsky et al., CLONING, EXPRESSION AND CHROMOSOMAL MAPPING OF HUMAN LYSOSOMAL SIALIDASE AND CHARACTERIZATION OF MUTATIONS IN SIALIDOSIS, Nature genetics, 15(3), 1997, pp. 316-320
ASSOCIATION OF N-ACETYLGALACTOSAMINE-6-SULFATE SULFATASE WITH THE MULTIENZYME LYSOSOMAL COMPLEX OF BETA-GALACTOSIDASE, CATHEPSIN-A, AND NEURAMINIDASE - POSSIBLE IMPLICATION FOR INTRALYSOSOMAL CATABOLISM OF KERATAN SULFATE
Authors: PSHEZHETSKY AV POTIER M
Citation: Av. Pshezhetsky et M. Potier, ASSOCIATION OF N-ACETYLGALACTOSAMINE-6-SULFATE SULFATASE WITH THE MULTIENZYME LYSOSOMAL COMPLEX OF BETA-GALACTOSIDASE, CATHEPSIN-A, AND NEURAMINIDASE - POSSIBLE IMPLICATION FOR INTRALYSOSOMAL CATABOLISM OF KERATAN SULFATE, The Journal of biological chemistry, 271(45), 1996, pp. 28359-28365
COMPARATIVE MODELING OF SUBSTRATE-BINDING IN THE S-1' SUBSITE OF SERINE CARBOXYPEPTIDASES FROM YEAST, WHEAT, AND HUMAN
Authors: ELSLIGER MA PSHEZHETSKY AV VINOGRADOVA MV SVEDAS VK POTIER M
Citation: Ma. Elsliger et al., COMPARATIVE MODELING OF SUBSTRATE-BINDING IN THE S-1' SUBSITE OF SERINE CARBOXYPEPTIDASES FROM YEAST, WHEAT, AND HUMAN, Biochemistry, 35(47), 1996, pp. 14899-14909
HUMAN LYSOSOMAL BETA-GALACTOSIDASE-CATHEPSIN A COMPLEX - DEFINITION OF THE BETA-GALACTOSIDASE-BINDING INTERFACE ON CATHEPSIN-A
Authors: PSHEZHETSKY AV ELSLIGER MA VINOGRADOVA MV POTIER M
Citation: Av. Pshezhetsky et al., HUMAN LYSOSOMAL BETA-GALACTOSIDASE-CATHEPSIN A COMPLEX - DEFINITION OF THE BETA-GALACTOSIDASE-BINDING INTERFACE ON CATHEPSIN-A, Biochemistry, 34(8), 1995, pp. 2431-2440
CONTINUOUS SPECTROPHOTOMETRIC ASSAY OF HUMAN LYSOSOMAL CATHEPSIN-A PROTECTIVE PROTEIN IN NORMAL AND GALACTOSIALIDOSIS CELLS
Authors: PSHEZHETSKY AV VINOGRADOVA MV ELSLIGER MA ELZEIN F
Citation: Av. Pshezhetsky et al., CONTINUOUS SPECTROPHOTOMETRIC ASSAY OF HUMAN LYSOSOMAL CATHEPSIN-A PROTECTIVE PROTEIN IN NORMAL AND GALACTOSIALIDOSIS CELLS, Analytical biochemistry, 230(2), 1995, pp. 303-307
DIRECT AFFINITY PURIFICATION AND SUPRAMOLECULAR ORGANIZATION OF HUMANLYSOSOMAL CATHEPSIN-A
Authors: PSHEZHETSKY AV POTIER M
Citation: Av. Pshezhetsky et M. Potier, DIRECT AFFINITY PURIFICATION AND SUPRAMOLECULAR ORGANIZATION OF HUMANLYSOSOMAL CATHEPSIN-A, Archives of biochemistry and biophysics, 313(1), 1994, pp. 64-70
DEMONSTRATION OF ENZYME ASSOCIATIONS BY COUNTERMIGRATION ELECTROPHORESIS IN AGAROSE-GEL (VOL 219, PG 349, 1994)
Authors: ASHMARINA LI PSHEZHETSKY AV SPIVEY HO POTIER M
Citation: Li. Ashmarina et al., DEMONSTRATION OF ENZYME ASSOCIATIONS BY COUNTERMIGRATION ELECTROPHORESIS IN AGAROSE-GEL (VOL 219, PG 349, 1994), Analytical biochemistry, 222(2), 1994, pp. 520-520
DEMONSTRATION OF ENZYME ASSOCIATIONS BY COUNTERMIGRATION ELECTROPHORESIS IN AGAROSE-GEL
Authors: ASHMARINA LI PSHEZHETSKY AV SPIVEY HO POTIER M
Citation: Li. Ashmarina et al., DEMONSTRATION OF ENZYME ASSOCIATIONS BY COUNTERMIGRATION ELECTROPHORESIS IN AGAROSE-GEL, Analytical biochemistry, 219(2), 1994, pp. 349-355
HUMAN GLYCOSIDASES REVERSED MICELLAR SYSTEM - PROPERTIES AND KINETICS
Authors: PSHEZHETSKY AV BEYER EM BUNEEVA OA VINOGRADOVA MV LEVASHOV AV WIEDERSCHAIN GY
Citation: Av. Pshezhetsky et al., HUMAN GLYCOSIDASES REVERSED MICELLAR SYSTEM - PROPERTIES AND KINETICS, Bioorganiceskaa himia, 19(2), 1993, pp. 161-173
STOICHIOMETRY OF THE HUMAN LYSOSOMAL CARBOXYPEPTIDASE-BETA-GALACTOSIDASE COMPLEX
Authors: PSHEZHETSKY AV POTIER M
Citation: Av. Pshezhetsky et M. Potier, STOICHIOMETRY OF THE HUMAN LYSOSOMAL CARBOXYPEPTIDASE-BETA-GALACTOSIDASE COMPLEX, Biochemical and biophysical research communications, 195(1), 1993, pp. 354-362
Risultati: 1-13 |