Citation: G. Uhlhorndierks et al., HOW DOES NATURE CLEAVE SULFURIC-ACID ESTERS - A NOVEL POSTTRANSLATIONAL MODIFICATION OF SULFATASES, ANGEWANDTE CHEMIE-INTERNATIONAL EDITION, 37(18), 1998, pp. 2453-2455
Authors:
REICHELT J
DORING T
SANDHOFF K
SCHNETZ E
FARTASCH M
MAGIN TM
Citation: J. Reichelt et al., EXPRESSION OF A TRUNCATED KERATIN-10 ALTERS TERMINAL DIFFERENTIATION OF MOUSE EPIDERMIS, Molecular biology of the cell, 9, 1998, pp. 955-955
Authors:
BEKTAS M
DULLIN Y
WIEDER T
KOLTER T
SANDHOFF K
BROSSMER R
IHRIG P
ORFANOS CE
GEILEN CC
Citation: M. Bektas et al., INDUCTION OF APOPTOSIS BY SYNTHETIC CERAMIDE ANALOGS IN THE HUMAN KERATINOCYTE CELL-LINE HACAT, Experimental dermatology, 7(6), 1998, pp. 342-349
Authors:
LI CM
HONG SB
KOPAL G
HE XX
LINKE T
HOU WS
KOCH J
GATT S
SANDHOFF K
SCHUCHMAN EH
Citation: Cm. Li et al., CLONING AND CHARACTERIZATION OF THE FULL-LENGTH CDNA AND GENOMIC SEQUENCES ENCODING MURINE ACID CERAMIDASE, Genomics, 50(2), 1998, pp. 267-274
Authors:
BREEN KC
POTRATZ A
GEORGOPOULOU N
SANDHOFF K
Citation: Kc. Breen et al., THE GENERATION AND CHARACTERIZATION OF A RAT NEURAL CELL-LINE OVEREXPRESSING THE ALPHA-2,6(N) SIALYLTRANSFERASE, Glycoconjugate journal, 15(2), 1998, pp. 199-202
Authors:
HIESBERGER T
HUTTLER S
ROHLMANN A
SCHNEIDER W
SANDHOFF K
HERZ J
Citation: T. Hiesberger et al., CELLULAR UPTAKE OF SAPOSIN (SAP) PRECURSOR AND LYSOSOMAL DELIVERY BY THE LOW-DENSITY-LIPOPROTEIN RECEPTOR-RELATED PROTEIN (LRP), EMBO journal (Print), 17(16), 1998, pp. 4617-4625
Authors:
BARTELSEN O
LANSMANN S
NETTERSHEIM M
LEMM T
FERLINZ K
SANDHOFF K
Citation: O. Bartelsen et al., EXPRESSION OF RECOMBINANT HUMAN ACID SPHINGOMYELINASE IN INSECT SF21 CELLS - PURIFICATION, PROCESSING AND ENZYMATIC CHARACTERIZATION, Journal of biotechnology, 63(1), 1998, pp. 29-40
Citation: T. Kolter et K. Sandhoff, GLYCOSPHINGOLIPID DEGRADATION AND ANIMAL-MODELS OF GM2-GANGLIOSIDOSES, Journal of inherited metabolic disease, 21(5), 1998, pp. 548-563
Authors:
LIU YJ
SUZUKI K
REED JD
GRINBERG A
WESTPHAL H
HOFFMANN A
DORING T
SANDHOFF K
PROIA RL
Citation: Yj. Liu et al., MICE WITH TYPE-2 AND TYPE-3 GAUCHER-DISEASE POINT MUTATIONS GENERATEDBY A SINGLE INSERTION MUTAGENESIS PROCEDURE (SIMP), Proceedings of the National Academy of Sciences of the United Statesof America, 95(5), 1998, pp. 2503-2508
Authors:
LANDRIEU P
BLANCHE S
VANIER MT
METRAL S
HUSSON B
SANDHOFF K
FISCHER A
Citation: P. Landrieu et al., BONE-MARROW TRANSPLANTATION IN METACHROMATIC LEUKODYSTROPHY CAUSED BYSAPOSIN-B DEFICIENCY - A CASE-REPORT WITH A 3-YEAR FOLLOW-UP PERIOD, The Journal of pediatrics, 133(1), 1998, pp. 129-132
Authors:
NORFLUS F
TIFFT CJ
MCDONALD MP
GOLDSTEIN G
CRAWLEY JN
HOFFMANN A
SANDHOFF K
SUZUKI K
PROIA RL
Citation: F. Norflus et al., BONE-MARROW TRANSPLANTATION PROLONGS LIFE-SPAN AND AMELIORATES NEUROLOGIC MANIFESTATIONS IN SANDHOFF DISEASE MICE, The Journal of clinical investigation, 101(9), 1998, pp. 1881-1888
Citation: G. Wilkening et al., LYSOSOMAL DEGRADATION ON VESICULAR MEMBRANE SURFACES - ENHANCED GLUCOSYLCERAMIDE DEGRADATION BY LYSOSOMAL ANIONIC LIPIDS AND ACTIVATORS, The Journal of biological chemistry, 273(46), 1998, pp. 30271-30278
Authors:
VANECHTENDECKERT G
GIANNIS A
SCHWARZ A
FUTERMAN AH
SANDHOFF K
Citation: G. Vanechtendeckert et al., L-METHYLTHIODIHYDROCERAMIDE, A NOVEL ANALOG OF DIHYDROCERAMIDE, STIMULATES SPHINGANINE DEGRADATION RESULTING IN DECREASED DE-NOVO SPHINGOLIPID BIOSYNTHESIS, The Journal of biological chemistry, 273(2), 1998, pp. 1184-1191
Citation: K. Sandhoff et T. Kolter, PROCESSING OF SPHINGOLIPID ACTIVATOR PROTEINS AND THE TOPOLOGY OF LYOSOMAL DIGESTION, Acta Biochimica Polonica, 45(2), 1998, pp. 373-384
Authors:
SCHICK A
SCHWARZMANN G
KOLTER T
SANDHOFF K
Citation: A. Schick et al., SYNTHESIS OF TRITIUM-LABELED PHOSPHONATE ANALOGS OF SPHINGANINE-1-PHOSPHATE, Journal of labelled compounds & radiopharmaceuticals, 39(5), 1997, pp. 441-451
Authors:
BURKHARDT JK
HUTTLER S
KLEIN A
MOBIUS W
HABERMANN A
GRIFFITHS G
SANDHOFF K
Citation: Jk. Burkhardt et al., ACCUMULATION OF SPHINGOLIPIDS IN SAP-PRECURSOR (PROSAPOSIN)-DEFICIENTFIBROBLASTS OCCURS AS INTRALYSOSOMAL MEMBRANE STRUCTURES AND CAN BE COMPLETELY REVERSED BY TREATMENT WITH HUMAN SAP-PRECURSOR, European journal of cell biology, 73(1), 1997, pp. 10-18
Authors:
LIU YJ
HOFFMANN A
GRINBERG A
WESTPHAL H
MCDONALD MP
MILLER KM
CRAWLEY JN
SANDHOFF K
SUZUKI K
PROIA RL
Citation: Yj. Liu et al., MOUSE MODEL OF G(M2) ACTIVATOR DEFICIENCY MANIFESTS CEREBELLAR PATHOLOGY AND MOTOR IMPAIRMENT, Proceedings of the National Academy of Sciences of the United Statesof America, 94(15), 1997, pp. 8138-8143
Authors:
VANECHTENDECKEN G
ZSCHOCHE A
BAR T
SCHMIDT RR
RATHS A
HEINEMANN T
SANDHOFF K
Citation: G. Vanechtendecken et al., CIS-4-METHYLSPHINGOSINE-1-PHOSPHATE AS A POTENTIAL METABOLICALLY STABLE MIMETIC OF SPHINGOSINE-1-PHOSPHATE ACTIVITY, Journal of neurochemistry, 69, 1997, pp. 18-18
Citation: K. Sandhoff et al., PROCESSING OF SPHINGOLIPID ACTIVATOR PROTEINS AND THE TOPOLOGY OF LYSOSOMAL DIGESTION, Journal of neurochemistry, 69, 1997, pp. 122-122
Authors:
VANECHTENDECKERT G
ZSCHOCHE A
BAR T
SCHMIDT RR
RATHS A
HEINEMANN T
SANDHOFF K
Citation: G. Vanechtendeckert et al., CIS-4-METHYLSPHINGOSINE-1-PHOSPHATE AS A POTENTIAL METABOLICALLY STABLE MIMETIC OF SPHINGOSINE-1-PHOSPHATE ACTIVITY, Journal of neurochemistry, 69, 1997, pp. 210-210