ATYPICAL MESOBLASTIC NEPHROMAS WITH METASTASES AT DIAGNOSIS

The diagnosis of a metastatic kidney tumor arising in a 2-month infant is discussed between atypical mesoblastic distant metastases, their l ocation in bone marrow, liver and thoracic soft tissues, and their ass ociation with myelofibrosis set up an original clinical presentation w hich seems to have never been described elsewhere. Treatment strategy with surgery of the primary followed by a polychemotherapy combining v incristin-etoposide-ifosfamide and the short term follow-up are report ed.