ADRENAL-TUMORS IN BECKWITH-WIEDEMANN SYND ROME - REPORT OF A CASE

A case of a neonate with Beckwith-Wiedemann syndrom is presented. Ante natal sonography detected a right adrenal cystic mass confirmed in pos tnatal which resolved spontaneously within 1 month. The child develope d an adrenal adenoma detected by abdominal sonography at six months of surveillance. The authors reveiw the different adrenal lesions possib ly associated with Beckwith-Wiedemann syndrom and specially the pseudo -tumorous lesions. The value of abdominal sonography in the neonatal p eriods and in the surveillance of children with Beckwith-Wiedemann syn drom is emphasized.