Lk. Tyler et al., DO INDIVIDUALS WITH WILLIAMS-SYNDROME HAVE BIZARRE SEMANTICS - EVIDENCE FOR LEXICAL ORGANIZATION USING AN ONLINE TASK, Cortex, 33(3), 1997, pp. 515-527
Williams syndrome, a neurodevelopmental disorder, has attracted a grea
t deal of debate concerning the purported intactness of language in th
e face of other serious cognitive deficits. As more in-depth studies o
f specific aspects of WS language have emerged, the notion of a preser
ved language module has been seriously challenged. Although WS vocabul
ary scores are often impressive, several investigators have claimed th
at WS semantics are aberrant. All studies hitherto have been based on
off-line experiments which necessarily involve metalinguistic processe
s. This clearly affects the performance of individuals with cognitive
deficits. We report here an on-line study probing the semantic structu
re of the WS lexicon, using a task - semantic priming - which minimise
s metalinguistic demands. We show that WS subjects display the same ta
xonomic/category and thematic/functional priming effects as normal con
trols. The results are discussed in terms of the differences between r
eceptive and expressive language, as well as the fact that although se
mantic memory and the automatic access to semantic information for ind
ividual words is normal in WS, the integration of semantic information
into sentence comprehension may be abnormal. The importance of online
tasks to highlight such differences is stressed.