CONGENITAL ECCRINE ANGIOMATOUS HAMARTOMA

Background Eccrine angiomatous hamartoma is an uncommon skill disease with vascular and sudoral components: less than thirty cases have been reported in the literature. Case report A 3.5 month-old female infant developed a painful angiomatous plaque on the abdomen which was first seen 15 days after birth. Histology showed numerous vessels and eccri ne sudoral glands in the dermis. Exeresis could nor be complete and wa s followed for 15 years. There has been a slight hyperpigmentation wit h localized hyperhidrosis over the plaque. This hypersudation confirms the diagnosis which could not be confirmed on the initial biopsies. D iscussion This case of congenital eccrine angiomatous hamartoma could only be diagnosed late in the clinical course. This is the first case report on the abdomen, 80 p. 100 of the previous reports were on the l imbs. After a 15 year follow-up, there was no progression of the hamar toma and pain regressed gradually. Without secondary development of lo calized hyperhidrosis, the diagnosis could nor have been made. Careful comparison oi pathology findings and clinical expression are essentia l for the diagnosis of eccrine angiomatous hamartoma.