FETAL AKINESIA DEFORMATION SEQUENCE IN A HIGHLY DEVELOPED ACARDIUS TWIN

We report a case of a holoacardius twin with extremely advanced develo pment of the head, face, upper and lower limbs in the absence of all t horacic and upper abdominal viscera and associated with intestinal and anal atresia. The malformed fetus also had craniofacial abnormalities , hydrops, cystic hygroma of the neck, arthrogryposis and pterygia. Th e monozygous co-twin was found to be normal. The association of acardi a with the typical characteristics of the fetal akinesia deformation s equence has not been previously described in the literature.