MEDULLOEPITHELIOMA OF THE OPTIC-NERVE HEAD

Medulloepithelioma of the optic nerve is a rare developmental tumor. W e describe a 2-year-old boy with profound loss of vision associated wi th a visible tumor of the optic nerve head in his left eye. A clinical ly diagnosed retinoblastoma necessitated left eye enucleation. The his topathological diagnosis was malignant medulloepithelioma that was inc ompletely resected. Further tumor resection was required, and the pati ent received adjunctive chemotherapy and radiotherapy. Four years afte r treatment, the patient has neither clinical nor radiological evidenc e of tumor.