A COMPLEX COMMUNICATING BRONCHOPULMONARY FOREGUT MALFORMATION - DIAGNOSTIC-IMAGING AND PATHOGENESIS

We report a newborn with an esophageal lung, a rare type of communicat ing bronchopulmonary foregut malformation (CBPFM). Associated findings included esophageal atresia, tracheoesophageal fistula (TEF) to the d istal esophagus, duodenal stenosis with annular pancreas, imperforate anus, vertebral anomalies and ambiguous genitalia. Radiologic evaluati on included chest radiographs, esophagrams, chest ultrasound and chest CT. After colostomy and surgical repair of duodenal stenosis and TEE a right thoracotomy was performed to treat an esophageal lung. Radiolo gic features of this unusual variant of CBPFM are presented. Accurate preoperative imaging diagnosis is essential for planning surgical trea tment of an esophageal lung.