Malignant clear cell hidradenoma is an uncommon tumor of eccrine sweat
gland origin that has a predilection for the head and neck. It is cha
racterized by an indolent growth pattern yet frequently recurs followi
ng surgical excision and has a high incidence of regional and distant
metastases. A case of recurrent malignant clear cell hidradenoma of th
e upper lip is presented. The lesion was treated with surgical excisio
n followed by radiotherapy. The literature on this rare lesion is revi
ewed and treatment strategies discussed. (C) 1994 John Wiley & Sons, I
nc.