A 12-YEAR-OLD CAUCASIAN boy presented with a thoracic myelopathy. Magn
etic resonance T1-weighted images revealed an enhancing lesion infiltr
ating the lower thoracic spinal cord to the level of the conus. Evalua
tion of the lesion by open biopsy revealed granulomatous angiitis of t
he spinal cord. Granulomatous angiitis is a rare vasculitic process th
at typically involves the brain and, less frequently, the spinal cord.
Diagnosis must be established early by histopathological examination
so that treatment with corticosteroids and/or cytotoxic agents may be
instituted. When left untreated, patients with granulomatous angiitis
of the spinal cord have developed fatal intracranial manifestations.