INFANTILE SCIMITAR SYNDROME WITH SEVERE PULMONARY-HYPERTENSION - SUCCESSFUL TREATMENT WITH COIL EMBOLIZATION OF THE SYSTEMIC ARTERIAL SUPPLY TO THE SEQUESTERED LUNG
Jp. Pfammatter et al., INFANTILE SCIMITAR SYNDROME WITH SEVERE PULMONARY-HYPERTENSION - SUCCESSFUL TREATMENT WITH COIL EMBOLIZATION OF THE SYSTEMIC ARTERIAL SUPPLY TO THE SEQUESTERED LUNG, Cardiology in the young, 7(4), 1997, pp. 454-457
Scimitar syndrome is a rare cardiopulmonary malformation. Presentation
in infancy is usually associated with pulmonary hypertension and seve
re symptoms. We discuss treatment of such an infant. Two abnormal syst
emic vessels supplying the sequestered lower part of the right lung we
re embolized using catheter-inserted coils. The patent arterial duct w
as surgically ligated. These procedures resulted in a significant redu
ction of the shunt and the level of pulmonary hypertension, as well as
in an impressive improvement of symptoms.