INFANTILE SCIMITAR SYNDROME WITH SEVERE PULMONARY-HYPERTENSION - SUCCESSFUL TREATMENT WITH COIL EMBOLIZATION OF THE SYSTEMIC ARTERIAL SUPPLY TO THE SEQUESTERED LUNG

Citation
Jp. Pfammatter et al., INFANTILE SCIMITAR SYNDROME WITH SEVERE PULMONARY-HYPERTENSION - SUCCESSFUL TREATMENT WITH COIL EMBOLIZATION OF THE SYSTEMIC ARTERIAL SUPPLY TO THE SEQUESTERED LUNG, Cardiology in the young, 7(4), 1997, pp. 454-457
Citations number
9
Categorie Soggetti
Pediatrics,"Cardiac & Cardiovascular System
Journal title
ISSN journal
10479511
Volume
7
Issue
4
Year of publication
1997
Pages
454 - 457
Database
ISI
SICI code
1047-9511(1997)7:4<454:ISSWSP>2.0.ZU;2-F
Abstract
Scimitar syndrome is a rare cardiopulmonary malformation. Presentation in infancy is usually associated with pulmonary hypertension and seve re symptoms. We discuss treatment of such an infant. Two abnormal syst emic vessels supplying the sequestered lower part of the right lung we re embolized using catheter-inserted coils. The patent arterial duct w as surgically ligated. These procedures resulted in a significant redu ction of the shunt and the level of pulmonary hypertension, as well as in an impressive improvement of symptoms.