INFANTILE SCIMITAR SYNDROME WITH SEVERE PULMONARY-HYPERTENSION - SUCCESSFUL TREATMENT WITH COIL EMBOLIZATION OF THE SYSTEMIC ARTERIAL SUPPLY TO THE SEQUESTERED LUNG

Scimitar syndrome is a rare cardiopulmonary malformation. Presentation in infancy is usually associated with pulmonary hypertension and seve re symptoms. We discuss treatment of such an infant. Two abnormal syst emic vessels supplying the sequestered lower part of the right lung we re embolized using catheter-inserted coils. The patent arterial duct w as surgically ligated. These procedures resulted in a significant redu ction of the shunt and the level of pulmonary hypertension, as well as in an impressive improvement of symptoms.