UNUSUAL PRESENTATION OF AMNIOTIC BAND SYNDROME

Citation
R. Nahum et al., UNUSUAL PRESENTATION OF AMNIOTIC BAND SYNDROME, Journal of ultrasound in medicine, 16(11), 1997, pp. 759-761
Citations number
8
Categorie Soggetti
Acoustics,"Radiology,Nuclear Medicine & Medical Imaging
ISSN journal
02784297
Volume
16
Issue
11
Year of publication
1997
Pages
759 - 761
Database
ISI
SICI code
0278-4297(1997)16:11<759:UPOABS>2.0.ZU;2-A
Abstract
ABS refers to a spectrum of asymmetric nonembryologic disruptive abnor malities of various fetal parts involving Limbs, the craniofacial regi on, and the trunk attributed to fibrous bands.(1) Most authors agree w ith the hypothesis elaborated in 1968 by Torpin, who thought that ABS was caused by antenatal rupture of the amnion, leading to entrapment o f fetal parts by fibroid bands.(2) The prevalence of ABS is one in 130 0 live births and is considered a sporadic event. Prenatal diagnosis o f cases of ABS made in the past was based on sonographic visualization of either amniotic sheets or bands associated with fetal deformities. (3,4) Although most of the anomalies associated with ABS are presented as a disruption of fetal body parts, including ring constriction of l imbs, abdominal wall defects,anencephaly, encephalocele, calvarial and facial defects, scoliosis, and spina bifida, ABS infrequently has a d ifferent picture. We report on a rare and unusual case of ABS diagnose d at 16 weeks' gestation, causing extreme exaggeration of cervicothora cic lordosis.