MUCOPOLYSACCHARIDOSIS-III (SANFILIPPO-SYNDROME) TYPE-B - CRANIAL IMAGING IN 2 CASES

Authors
PETITTI N HOLDER CA WILLIAMS DW
Citation
N. Petitti et al., MUCOPOLYSACCHARIDOSIS-III (SANFILIPPO-SYNDROME) TYPE-B - CRANIAL IMAGING IN 2 CASES, Journal of computer assisted tomography, 21(6), 1997, pp. 897-899
Citations number
14
Categorie Soggetti
Radiology,Nuclear Medicine & Medical Imaging
Journal title
Journal of computer assisted tomography → ACNP
ISSN journal
03638715
Volume
21
Issue
6
Year of publication
1997
Pages
897 - 899
Database
ISI
SICI code
0363-8715(1997)21:6<897:M(T-CI>2.0.ZU;2-0
Abstract
We present the imaging findings in two patients with mucopolysaccharid osis III (Sanfilippo syndrome) type B, both with arachnoid cysts. We p ostulate that the deposition of glycosaminoglycans in the meninges may impair CSF flow and explain the development of arachnoid cysts also n oted in patients with other forms of mucopolysaccharidoses.