Dnj. Ricketts et al., KINDLER-SYNDROME - A RARE CAUSE OF DESQUAMATIVE LESIONS OF THE GINGIVA, Oral surgery, oral medicine, oral pathology, oral radiology and endodontics, 84(5), 1997, pp. 488-491
Citations number
11
Categorie Soggetti
Pathology,Surgery,"Dentistry,Oral Surgery & Medicine
Kindler syndrome is a rare syndrome with cutaneous and intraoral manif
estations. It has been suggested that there is an overlap between this
syndrome and another called Weary syndrome. Only 68 cases of Weary an
d Kindler syndromes have been reported, with fewer solely attributed t
o Kindler syndrome. The salient cutaneous features are neonatal bullae
, poikilodermal photosensitivity, and acral atrophy. This article pres
ents the clinical intraoral findings of two siblings of consanguineous
descent diagnosed as having Kindler syndrome. Both had an erythematou
s and erosive appearance of the gingiva; one sibling had poor oral hyg
iene and a rapidly progressive form of periodontal disease; the other,
whose oral hygiene was acceptable, had no detectable bone loss.