SYNCHRONOUS OCCURRENCE OF WILMS-TUMOR AND GANGLIONEUROBLASTOMA IN A CHILD WITH NEUROFIBROMATOSIS

A 2-year-old male with neurofibromatosis who had a Wilms tumor of the right kidney and an ipsilateral adrenal ganglioneuroblastoma is report ed. Both tumors were completely removed and no recurrence occurred for 4 years after completion of the therapy. In a review of the literatur e, the prognosis of neurofibromatosis with these embryonal tumors is n ot satisfactory due to development of secondary tumors and disseminate d metastases of the tumors. The synchronous occurrence of Wilms tumor and neuroblastoma in neurofibromatosis is extremely rare and this may be the first report in the world.