A CASE OF MENINGIOANGIOMATOSIS WITHOUT VON RECKLINGHAUSENS DISEASE - REPORT OF A CASE AND REVIEW OF 13 CASES

Meningioangiomatosis is rare disease and is classified as hamartoma in central neurofibromatosis. Unlike most cases of meningioangiomatosis, the very rare case reported here was not associated with von Reckling hausen's disease. We could find only 12 previous cases reported in the literature. A review was carried out of the clinical features, imagin g characteristics, and histopathological findings in those 12 plus our s for a total 13 cases. Several types of convulsion were identified as clinical symptoms in 11 of the 13 cases. They were treated surgically . Prognosis was satisfactory in most cases. Proliferation of small blo od vessels accompanied by endothelial cells with glial tissue as backg round and proliferation of fibroblasts or meningothelial cells in the perivascular space were observed to be the most frequent histopatholog ical features.