G. Rosenn et al., ASSOCIATION OF WILMS-TUMOR AND INTRACRANIAL HEMORRHAGE DUE TO ARTERIOVENOUS MALFORMATION, Child's nervous system, 10(2), 1994, pp. 135-137
A high incidence of congenital malformations associated with Wilms' tu
mor has been recognized lately. Aniridia, hemihypertrophy, and urinary
tract anomalies are among the most frequently reported. Anomalies of
the central nervous system associated with Wilms' tumor are rare. We r
eport a previously healthy 4-year-old girl who presented with an intra
cranial hemorrhage secondary to a ruptured arteriovenous malformation.
A routine abdominal examination revealed a large right-sided Wilms' t
umor. The question generated by the coexistence of these two uncommon
disorders in one individual is whether there is a genetic or other rel
ationship between them, or whether this is merely a coincidental occur
rence. The question at this point is unanswered and must await demonst
ration of additional, similar cases.