Sj. Orlow et al., INCREASED RISK OF SYMPTOMATIC HEMANGIOMAS OF THE AIRWAY IN ASSOCIATION WITH CUTANEOUS HEMANGIOMAS IN A BEARD DISTRIBUTION, The Journal of pediatrics, 131(4), 1997, pp. 643-646
We evaluated the frequency of an association of cutaneous cervicofacia
l hemangiomas in a ''beard'' distribution (including the preauricular
areas, chin, anterior neck, and lower lip) with symptomatic hemangioma
s of the upper airway or subglottic areas. Of 529 patients seen, 187 w
ere pediatric patients with hemangiomas of the head and neck. Sixteen
of the 187 patients (8.5%) had cutaneous lesions with a beard distribu
tion, with a score of 4 or greater. Ten of these 16 (63%) patients had
some degree of symptomatic airway involvement, and four of the 10 (40
%) required tracheotomy. The presence of cutaneous hemangiomas in a be
ard distribution should alert the evaluating physician to the potentia
l association of upper airway or subglottic involvement.