TUMOR OF THE BROAD LIGAMENT IN VON-HIPPEL-LINDAU-DISEASE OF PROBABLE MULLERIAN ORIGIN

A rare neoplasm seen in women with von Hippel-Lindau disease is the pa pillary cystadenoma of the broad ligament. only three cases of which h ave been reported. All three exhibited characteristic histologic featu res identical to those of epididymal tumors that occur in affected pat ients, and were presumed to be of wolffian origin. This is the case of a broad ligament tumor in a woman with von Hippel-Lindau disease that had features more consistent with a mullerian rather than wolffian or igin. This is the first report of a broad Ligament tumor of probable m ullerian origin in von Hippel-Lindau disease.