CYSTIC RENAL LYMPHANGIECTASIA - A DISTINCTIVE CLINICOPATHOLOGICAL ENTITY IN THE PEDIATRIC AGE GROUP

This report describes the features of unilateral cystic renal lymphang iectasia in a 2-year-old child who presented with hypertension, massiv e ascites, a left flank mass, and no evidence of familial renal cystic disease. The child became normotensive and is now asymptomatic more t han 3 years after surgery. The clinical presentation and diffuse patho logic involvement are similar to findings for the few pediatric patien ts with cystic lymphangiectasia described in the literature and appear distinct from the more localized form of the disease seen in adults.