CARDIOMYOPATHY - A LATE COMPLICATION OF HEMOLYTIC-UREMIC SYNDROME

This report describes a child who presented with classic hemolytic ure mic syndrome (HUS) and 4 months later developed a life-threatening but reversible cardiomyopathy with global cardiac dysfunction and a left ventricular ejection fraction of 14%. There was no evidence of electro lyte abnormalities, anemia, hypertension, severe fluid overload, or vi ral infection, Endomyocardial biopsies were consistent with a dilated cardiomyopathy, This paper highlights the importance of considering th e diagnosis of associated cardiomyopathy when presenting with late-ons et edema following HUS.