HEMINASAL-APLASIA - A CASE-REPORT AND REVIEW OF THE LITERATURE OF THELAST 25 YEARS

We report a child with right-sided heminasal aplasia in combination wi th anomalies of the right eye and maxilla. Unilateral aplasia of the n ose is a rare congenital malformation. It is often associated with oth er malformations of the facial region, including abnormalities of the eye and lacrimal system, proboscis lateralis? and facial bone malforma tions. The eye anomalies in our patient consisted of microphthalmia wi th blepharophimosis and coloboma of the iris, retina and upper eyelid. Also hypoplasia of the lacrimal apparatus and right maxilla, and a ru dimentary alveolar cleft on the same side were present. The embryologi cal development of the midface can explain this association of anomali es.