CONGENITAL DEFICIENCY OF THE FIBULA WITH IPSILATERAL ILIAC HORN AND ABSENCE OF THE KIDNEY

Congenital deficiency of the fibula is sometimes accompanied by femora l hypoplasia, genu valgum, patellar a/hypoplasia or dislocation, tibia l bowing, foot deformity and toe deficiency in the affected limb. 'Ili ac horns' are bony projections extending posterolaterally from the ili um and considered to be pathognomonic of nail-patella syndrome. We rep ort a 5-year-old Japanese girl with congenital complete deficiency of the left fibula, ipsilateral iliac horn and absence of the left kidney .