AGGRESSIVE PAPILLARY TUMOR OF THE TEMPORAL BONE - DELAYED EXTENSIVE RECURRENCE FOLLOWING RADIATION-THERAPY

Endolymphatic sac tumors have been characterized as aggressive papilla ry tumors of the temporal lobe, exhibiting extensive bony destruction and intracranial extension. This report describes the delayed recurren ce of an aggressive endolymphatic sac tumor following full course radi otherapy many years previously. The discussion reviews the current lit erature an these aggressive lesions with emphasis on clinical presenta tion, diagnosis, radio-graphic and histologic appearance acid manageme nt. This case highlights the need for total surgical excision in the m anagement of these lesions. Radiotherapy as primary management may slo w tumor growth but does not appear to be an appropriate therapeutic mo dality for cure.