PRENATAL DETECTION OF A CONGENITAL PANCREATIC CYST AND BECKWITH-WIEDEMANN-SYNDROME

We report a case of congenital pancreatic cyst detected prenatally by ultrasound in a fetus with evidence for a diagnosis of Beckwith-Wieder mann syndrome (BWS). Neonatal hypoglycaemia was prevented. The cyst wa s managed by internal drainage. This is the second reported case of BW S associated with pancreatic cystic dysplasia and the first time that this association has been detected prenatally. Differential diagnosis of cystic abdominal lesions occurring in utero should take pancreatic cysts into consideration. This case suggests that pancreatic cysts sho uld be included in the BWS phenotype. (C) 1997 by John Wiley & Sons, L td.