MULTIPLE SUPRATENTORIAL AND INFRATENTORIA L LACUNES IN PSEUDOXANTHOMAELASTICUM

Pseudoxanthoma elasticum (Gronblad-Strandberg syndrome) is a rare here ditary disorder of connective tissue. Neurovascular manifestations are caused by occlusive alterations of the small and medium-sized arterie s. We describe a 60-year old man with cerebral micro-angiopathy, who s uffered recurrent ischaemic strokes of the brainstem. The disease can be diagnosed by its characteristic cutaneous features.