DIFFUSE CHOROIDAL HEMANGIOMA - REPORT OF A CLINICOPATHOLOGICAL STUDY IN A 4-YEAR-OLD BOY

The authors examined the clinicopathologic features of a 4-year-old bo y with a diffuse choroidal hemangioma, yet without any features of the Sturge-Weber syndrome. The tumor occurred as a grayish intraocular ma ss with an overlying retinal detachment and was highly reflective in t he ultrasonic examination. After contrast, the CT scan revealed diffus e thickening of the ocular wall associated with an enhanced irregular orbital mass. The pathologic examination revealed a cavernous hemangio ma involving the entire choroid with extrascleral extension, Diffuse c horoidal hemangioma occurring in childhood and unrelated to the Sturge -Weber syndrome is a rare condition that should be included in the dif ferential diagnosis of retinoblastoma.