SUPRATENTORIAL ECTOPIC EPENDYMOMA

Background: Ependymomas usually arise from the ventricular surface, Me thods: We report an 11-year-old female who presented with a supratento rial ectopic ependymoma, Results: The patient presented with a two-mon th-history of progressive headache, nausea and vomiting. Examination r evealed papilledema, horizontal nystagmus, diplopia on upward gaze, an d right pronator drift, CT scan showed an enhancing left precentral su bcortical lesion measuring 3 cm in diameter with associated edema and mass effect, Its medial border was located 3 cm from the ependymal sur face of the ventricle, A firm tumour was dissected from the centrum se miovale white matter, and removed in tote as confirmed on MRI. Patholo gical examination revealed histological, immuno-histochemical and elec tron microscopic features consistent with an ependymoma, Spine MRI and bone marrow aspirate, as well as lumbar puncture of cytology failed t o show any dissemination. Conclusion: From the literature review, this represents an exceptional ependymoma located at the distance from the ventricular system or cisterns. Different pathogenic alternatives are discussed.