DESMOID TUMOR OF THE ULNA IN A PATIENT WITH NEUROFIBROMATOSIS

Authors
Citation
Ad. Mih, DESMOID TUMOR OF THE ULNA IN A PATIENT WITH NEUROFIBROMATOSIS, The Journal of hand surgery, 20A(6), 1995, pp. 1007-1010
Citations number
NO
Categorie Soggetti
Orthopedics,Surgery
Journal title
ISSN journal
03635023
Volume
20A
Issue
6
Year of publication
1995
Pages
1007 - 1010
Database
ISI
SICI code
0363-5023(1995)20A:6<1007:DTOTUI>2.0.ZU;2-9
Abstract
Desmoplastic fibroma is a rare benign tumor of bone and fibrous connec tive tissue, First described by Jaffe(1) in 1958 as a benign intraosse ous fibrous tumor, it is characterized by abundant collagen formation with histologic features resembling the desmoid tumor of the abdominal wall. The appearance on x-ray films is characterized by osteolytic ch anges arising centrally from bone with expanding radiolucency and cort ical thinning, Periosteal reaction is not present and there is marked bone destruction, most often in the metaphysis.(2) Desmoid tumors have rarely been reported in the upper extremity, Prior authors have repor ted on cases involving the hand as well as the bones of the forearm.(3 -7) A review of the literature finds less than 20 cases of desmoid tum ors involving the upper extremity. The present report describes a desm oplastic fibroma occurring in the ulna of a skeletally immature indivi dual with neurofibromatosis.