An aneurysm of the sinus of Valsalva (SVA) is a relatively rare congen
ital anomaly accounting for less than 1% of operative cases requiring
cardiopulmonary bypass for congenital heart disease.(1) It may be clin
ically silent for many years, causing symptoms only when mechanical ob
struction or rupture occurs, and it appears to be more common in Orien
tals and in men.(2-4) The hemodynamic consequences of rupture may lead
to rapidly progressive heart failure; thus rapid and accurate diagnos
is is essential. The essential anatomic defect is a failure of fusion
between the aortic media and the heart at the level of the annulus fib
rosis of the aortic valve.(5) This failure allows weakening of the SVA
wall and eventual development of an aneurysm. Doppler echocardiograph
y has greatly enhanced the capability for diagnosis of an SVA and its
associated lesions. The current spatial resolution of echocardiography
and color flow mapping has the potential for detailed anatomic analys
is of SVA and its associated defects similar to previous necropsy seri
es.(5, 6) This study evaluates the efficacy of Doppler echocardiograph
y for detailed anatomic analysis of a consecutive series of patients w
ith SVA, all of whom had surgical confirmation of the anatomic abnorma
lity.