INFANTILE MYOFIBROMATOSIS - A CASE-REPORT

Infantile myofibromatosis is a rare mesenchymal disorder of infancy ch aracterized by the formation of tumors in the skin, muscle, viscera, b one and subcutaneous tissue. The etiology of the disorder is unknown. We describe here a newborn with multiple infantile myofibromatosis, pe ritonitis and intestinal perforation. Surgery revealed multiple intest inal obstructions and jejunal perforation due to intestinal tumors; co nsequently, a jejunostomy was performed. The patient was maintained on total parenteral nutrition and oral semiliquid infant formula for two months, however he died due to multiple attacks of diarrhea and septi cemia.