A. Mirode et al., PULMONARY-HYPERTENSION ASSOCIATED WITH PO RTAL-HYPERTENSION - 2 CASESREPORTS, Archives des maladies du coeur et des vaisseaux, 88(11), 1995, pp. 1647-1650
The authors report the cases of two patients with pulmonary hypertensi
on associated with portal hypertension. This is a rare association wit
h a reported prevalence ranging from 0.25 to 0.73 %. The diagnosis of
portal hypertension preceded that of pulmonary hypertension by several
years. The physiopathological mechanism of the latter is not well kno
wn although several hypotheses have been proposed. Treatment is only s
ymptomatic. The prognosis is usually poor, the causes of death being r
elated to complications of liver failure and/or portal hypertension or
to those of pulmonary hypertension.