PRIMARY AL AMYLOIDOSIS REVEALED BY HORTON DISEASE

Primary systemic amyloidosis rarely affects the walls of small and med ium-sized vessels. We report a case of primary AL amyloidosis masquera ding as giant cell arteritis at the onset of the disease, revealed by the temporal arteritis biopsy, and successfully treated by corticother apy for three years. Histology of temporal arteritis confirms the diag nosis of amyloidosis (characteristic birefringence with Congo red). We discuss in this case the diagnosis of primary amyloidosis revealed by Horton disease, or the coincidental association of these two diseases .