Neurologic syndromes are among the more common extracardiac complicati
ons of congenital heart disease. Major advances in the surgical manage
ment of congenital heart disease have changed the neurologic risk prof
ile of this population. Recent focus has been on presumed intraoperati
ve cerebral injury and its prevention, and on neurologic dysfunction p
resenting in the early postoperative period. The more common complicat
ions in the postoperative patient include seizures and stroke; in addi
tion, movement disorders, such as choreoathetosis, present major chall
enges both in prevention and management. This article will focus on re
cent advances in our understanding of these problems, specifically the
ir clinical presentation and management. In addition, areas in need of
further investigation will be discussed.