SJOGRENS-SYNDROME PRESENTING AS HYPOKALEMIC PARALYSIS DUE TO DISTAL RENAL TUBULAR-ACIDOSIS

A 57-year-old woman presented with a flaccid paralysis, muscle tendern ess. and respiratory depression. Laboratory results demonstrated sever e hypokalemia with hyperchloremic metabolic acidosis and abnormally ac idified urine. The urinary anion gap was positive in the presence of a cidemia. thus establishing the diagnosis of distal renal tubular acido sis (DRTA). The patient fully recovered after potassium and alkali rep lacement. Further investigation revealed Sjogren's syndrome as the und erlying cause of DRTA.