A case of metastatic extrarenal, retroperitoneal Wilms tumor developed
in the right adrenal gland in a four-year-old boy is reported. Wilms
tumor should be considered in pediatric patients with a juxtarenal ret
roperitoneal mass and pulmonary and mediastinal metastases. Computed t
omography and ultrasonography are valuable for evaluating tumor spread
. Preoperative chemotherapy is helpful, The locations, pathologic feat
ures, and etiology of Wilms tum are discussed based on a review of the
literature.