We report the second known case of yolk sac tumour of the external aud
itory canal, occurring in an eight-month-old girl, The excised tumour
demonstrated histopathological and immunohistochemical features identi
cal to those of yolk sac tumours of gonadal origin, The tumour was ane
uploid by now cytometry. The patient received chemotherapy post-operat
ively and has had no evidence of disease 13 months after surgery.