BACKGROUND: Vulvar liposarcoma is rare. Three cases have been reported
since 1966. Primary sarcomas of the vulva constitute 1-2% of all vulv
ar malignancies. Because of their location and appearance, they may be
easily misdiagnosed as a more benign process. CASE: A 65-year-old, bl
ack woman had a vulvar lesion that appeared clinically to be a Barthol
in's gland abscess. The lesion was a soft tissue mass, was excised in
tote and was sent for pathologic study with a presumed diagnosis of li
poma. The pathology report indicated pleomorphic liposarcoma. CONCLUSI
ON: Only three prior cases of this disease have been reported. The cli
nician should heighten his or her awareness in a patient with a vulvar
mass. Early diagnosis is imperative for a favorable outcome.