SINUS NODE DYSFUNCTION IN TUBEROUS SCLEROSIS

Tuberous sclerosis is an autosomal dominant disease with potential for involvement of the skin, brain, lungs, kidneys, and heart. A case of prolonged sinus node pause and episodes of unresponsiveness in a 21-we ek-old infant with tuberous sclerosis is described. The infant subsequ ently underwent placement of an epicardial pacemaker. This case illust rates the importance of electrocardiographic studies in infants with t uberous sclerosis and seizure-like episodes.