An unusual case of an interatrial communication similar to a sinus ven
osus defect associated with an overriding pulmonary venous chamber is
reported. There was no direct connection of the pulmonary venous syste
m with either the superior vena cava or the low right atrium, as is us
ual with sinus venosus defects. This defect may represent the result o
f a sinus venosus defect associated with cor triatriatum.