In two patients who had Budd-Chiari syndrome secondary to carcinoma, t
he diagnosis was made intraoperatively at the time of emergency right
atrial clearance required for severe cardiovascular distress. Curative
resection was not possible and both patients died. As previously note
d in the literature, it is extremely difficult to relate carcinoma to
the origin of Budd-Chiari syndrome. Retro- and suprahepatic involvemen
t of the vena cava is associated with a very poor prognosis. Complete
resection of these tumors is the only potentially curative treatment.
We suggest ways to obtain a simple and early histologic diagnosis befo
re initiating appropriate and radical surgical treatment.