The classic appearance of porokeratosis is characterized by a hyperker
atotic annular rim that expands peripherally, leaving an atrophic cent
er. Linear porokeratosis is a variant with collections of such lesions
arranged in a linear fashion, usually corresponding to a dermatome or
Blaschko's lines. Ulcerations have rarely been reported in patients w
ith porokeratosis. We report an unusual case of linear porokeratosis a
t birth, with erosions and ulcerations of the face and lower extremity
, that eluded diagnosis for nearly a year. Porokeratosis should be con
sidered in the differential diagnosis of erosions in the newborn perio
d.