LATE, PAINFUL, SUBUNGUAL HYPERKERATOSIS IN INCONTINENTIA PIGMENTI

The postpubertal appearance of subungual, painful keratotic tumors is a rare feature of incontinentia pigmenti. A patient affected by incont inentia pigmenti developed subungual, painful, nontumoral, hyperkerato tic lesions of the hands at 10 years of age. The mildness of the subun gual lesions may be explained by the early stage of the disorder, but it is difficult to correlate the severity of the fingertip pain with t he absence of true tumoral swelling. To our knowledge this is the youn gest patient reported so far and the only one with a prepubertal expre ssion of this puzzling disorder.