UNILATERAL HEARING-LOSS DUE TO A RHABDOMYOMA IN A 6-YEAR-OLD CHILD

A case report of a six-year-old child is presented, who had had a unil ateral sensorineural hearing loss for several years. Because of impair ment in the ABR as well as in the caloric testing a MRI and CT scan we re performed. A 17 mm tumour in the cerebellopontine angle (CPA) was d etected, which after suboccipital surgery proved to be a rhabdomyoma. This tumour has not been described before in the CPA. Unilateral senso rineural hearing loss should, at all ages, be an indication for furthe r (radiodiagnostic) investigations.