CONGENITAL ANNULAR CONSTRICTING BAND - A CASE-REPORT WITH PSEUDOARTHROSIS AND REVIEW OF THE LITERATURE

A case of congenital annular constricting band syndrome with an open p seudarthrosis of the tibia and Fibula is reported. Ischemia, neurologi cal defect and major lymphoedema were present. The child had an emerge ncy treatment combining an external fixator and a one-stage resection of the constricting band: Bone union was obtained within 4 weeks and c omplete neurological recovery at 6 months. Long-term result, with real ignment and normal function, is satisfactory. A review of the literatu re is undertaken. Amputations are frequent, however pseudarthroses are rare. One-step treatment of the band has been proposed by certain aut hors. Neurological recovery is usual. The risk of ischemia favors an e arly surgical treatment.