THE BLAND-WHITE-GARLAND SYNDROME - CLINICAL PICTURE AND ANESTHESIOLOGICAL MANAGEMENT

We report a five-month-old infant with an impaired left ventricular ej ection fraction as a result of Bland-White-Garland-syndrome (BWGS). To tal intravenous anaesthesia with fentanyl and midazolam was used as th e anaesthetic technique. After aortic reimplantation of the left coron ary artery, weaning from cardiopulmonary bypass (CPB) was prolonged an d was only successfully managed with high dose noradrenaline, dopamine and dobutamine. Persistent myocardial dysfunction led to prolonged in tensive care treatment. Seven months after surgery, left ventricular f unction and clinical condition have improved significantly.