This study examined patients with known ventricular tachycardia after
repair of congenital heart disease to determine prognosis and identify
possible risk factors for sudden death. The charts of 76 patients see
n at Texas Children's Hospital between 1984 and 1989 with ventricular
tachycardia after repair of congenital heart disease were reviewed. Cl
inical and hemodynamic status were assessed. Mean age of primary repai
r was 7.7 years (0.3-29.3), and average follow-up was 11.3 years (0.3-
33.8). Of the ten patients who died, four died suddenly. Ten patients
(13%) experienced cardiac arrest, which occurred in 36% of patients wi
th 'poor', 17% with 'fair', and 3% with 'good' clinical status. All se
ven evaluated cardiac arrest patients had 'poor' hemodynamics, compare
d to 62% (28/45) of others. Although syncope was a common event (14/76
), no patient who arrested had prior syncope. Of the 20 patients who u
nderwent surgical revision, ventricular tachycardia persisted in 17. C
onclusions: (1) 13% of patients with ventricular tachycardia after the
repair of congenital heart disease experienced cardiac arrest. (2) No
cardiac arrest patient in this series had prior syncope, making this
a non-specific symptom. (3) Patients with clinical and catheterization
findings suggestive of the worst hemodynamics were most likely to hav
e cardiac arrest. (4) Surgical intervention did not prove successful i
n eliminating ventricular tachycardia or preventing cardiac arrest.